Piebaldism: A Brief Report

The word Piebaldism is derived from combination of two words Magpie (pie) and Bald eagle (bald). It is a rare autosomal dominant pigmentary disorder characterised by complete absence of melanocytes in affected areas of skin and hair. Its prevalence is less than one per 20000 individuals.

Characteristic triangular or diamond shaped depigmented macule in midline of forehead along with white forelock is present in affected individuals in majority of cases (90%). There is usually symmetrical involvement of ventral surface of trunk and middle part of extremities. These lesions are persistent and have a static course with characteristic distribution. We report this case in which multiple members of the same family were affected with variable expression of the disease.